ANIRIDIA
CONGENTIAL ANIRIDIA:
Aniridia means the absence of the iris (the coloured part of the eye that causes us to
call people
"blue-eyed" or "brown-eyed"). Although the iris appears to be absent
when examined, it has been shown what remains in cases
of aniridia is merely a thick collar of tissue around the
outer edge. The muscles which open and close the pupil are
absent.
Aniridia is a hereditary, developmental defect often associated with additional
anomalies. In some cases,
there may be a cataract (cloudiness of the lens), under-development of the fovea (the minute area in the centre of the macula which contains
the most closely packed cells for our finest sight),
persistent hyaloid artery (a vessel which normally disappears
before birth, but which can interfere with good vision when it persists after birth), and/or glaucoma (increased pressure within the eye).
Decreased visual acuity (poor resolution of detail), photophobia (extreme sensitivity to light) and field loss (decreased angle of vision) often result
from aniridia. Other losses are more likely consequences of the other defects
that may accompany aniridia.
Vision may fluctuate depending on lighting conditions and
glare. As a result, lighting conditions in the class will
need to be controlled. Teachers should not stand in front of a window or other light source when speaking to the student, and extra time to adapt to
changes in lighting should be allowed. Paper copies of
overhead transparencies or blackboard work can be helpful.
Adapted from "Aniridia" by G.H. Marshall and Low Vision by Nancy Levack
acquired aniridia:
This condition arises either from a latent congenital defect such as the Axenfeld Rieger (essential iris atrophy syndrome) or from injury to the eye in which all or part of the iris is damaged.